Impaired Lung BCAA Metabolism Promotes Ferroptosis and Resultant Pulmonary Arterial Hypertension-Associated Hepatopathy

Blake MJ, Hong J, Brownstein A, Rhodes CJ, Swietlik EM, Blake JC, Moon RA, Hartweck LM, Mendelson JB, Prisco SZ, Markowski T, Higgins L, Murray K, Guerrero C, Breuils-Bonnet S, Provencher S, Pepke-Zaba J, Toshner M, Wilkins M, Bonnet S, Prins KW. Impaired Lung BCAA Metabolism Promotes Ferroptosis and Resultant Pulmonary Arterial Hypertension-Associated Hepatopathy. JACC Basic Transl Sci. 2026 May 29;11(7):101573. doi: 10.1016/j.jacbts.2026.101573. Epub ahead of print. PMID: 42214135.


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